Primary Care

Diffuse Parenchymal Lung Disease

Questions discussed in this category

Do you ever consider tapering off steroid-sparing agents in patients with stable non-IPF ILD?

Do you perform routine interval screening for renal angiomyolipomas in patients with sporadic LAM?

How often do you monitor pulmonary function tests in patients with fibrotic lung disease?

Do you perform routine interval screening for pulmonary fibrosis in individuals who have been identified through genetic testing as being at risk for developing pulmonary fibrosis but don't exhibit any signs or symptoms?

Specifically considering individuals with known mutations in MUC5B, TERT/TERC, etc

2 Answers available

What is your approach to evaluation and management of GERD in a patient with IPF?

1 Answer available

What dose and duration of steroid therapy do you employ while starting mycophenolate in an outpatient with relatively stable CTD-ILD?

Do you ever start mycophenolate without steroids?

1 Answer available

Do you routinely perform genetic testing in patients presenting with pulmonary fibrosis who endorse a family history of fibrotic lung disease?

1 Answer available

Is there an age at which you consider not starting antifibrotic therapy in a patient with IPF?

1 Answer available

When do you screen for pulmonary hypertension in ILD patients?

1 Answer available

Papers discussed in this category

Pediatric neurology, 2021 Jul 24

Updated International Tuberous Sclerosis Complex Diagnostic Criteria and Surveillance and Management Recommendations.

Orphanet journal of rare diseases, 2014 Oct 03

Natural history of angiomyolipoma in lymphangioleiomyomatosis: implications for screening and surveillance.

The Lancet. Respiratory medicine, 2018-08

Analysis of protein-altering variants in telomerase genes and their association with MUC5B common variant status in patients with idiopathic pulmonary fibrosis: a candidate gene sequencing study.

Respir Med, 2011 Sep 13

Familial pulmonary fibrosis is the strongest risk factor for idiopathic pulmonary fibrosis.

Mayo Clin Proc, 2018 May 24

Short Telomere Syndromes in Clinical Practice: Bridging Bench and Bedside.

Respirology, 2021 Oct 06

Pulmonary fibrosis associated with telomere-related gene mutations: A complex inheritance.

N Engl J Med, 2021 Jan 13

Inhaled Treprostinil in Pulmonary Hypertension Due to Interstitial Lung Disease.

American journal of respiratory and critical care medicine, 2020 May 15

Interstitial Lung Disease in Relatives of Patients with Pulmonary Fibrosis.

BMJ open respiratory research, 2021 Jul

Fine crackles on chest auscultation in the early diagnosis of idiopathic pulmonary fibrosis: a prospective cohort study.

American journal of respiratory and critical care medicine, 2019 Jul 15

Clinical Effectiveness of Antifibrotic Medications for Idiopathic Pulmonary Fibrosis.

PloS one, 2022 Feb 03

Tolerability of nintedanib in the elderly with idiopathic pulmonary fibrosis: A single-center retrospective study.

Respiration; international review of thoracic diseases, 2022 Nov 10

Observational, Multicenter Study on the Efficacy, Tolerability, and Safety of Nintedanib in Patients with Idiopathic Pulmonary Fibrosis Older than 80 Years.

BMC pulmonary medicine, 2024 Dec 05

Evaluating the diagnostic and prognostic utility of serial KL-6 measurements in connective tissue disease patients at risk for interstitial lung disease: correlations with pulmonary function tests and high-resolution computed tomography.

The Lancet. Respiratory medicine, 2013-07

Anti-acid treatment and disease progression in idiopathic pulmonary fibrosis: an analysis of data from three randomised controlled trials.

The Lancet. Respiratory medicine, 2018-09

Laparoscopic anti-reflux surgery for the treatment of idiopathic pulmonary fibrosis (WRAP-IPF): a multicentre, randomised, controlled phase 2 trial.

The European respiratory journal, 2006 Jan

High prevalence of abnormal acid gastro-oesophageal reflux in idiopathic pulmonary fibrosis.

Primary Care

Diffuse Parenchymal Lung Disease

Questions discussed in this category

Papers discussed in this category

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