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How do you treat congenital paramyotonia symptoms?

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Mednet Member
Mednet Member
Neurology · University of Minnesota
  1. Avoid cold- and definitely do not exercise in cold.
  2. For the myotonia: mexiletine is my 1st line, if not tolerated or contraindicated, can use lamotrigine, or other sodium channel blockers like carbamazepine, lacosamide, or ranolazine.
  3. If the patient has coexistent hyperkalemic periodic paralysis, ...

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