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In a pediatric patient diagnosed with orbital sarcoidosis (dacryoadenitis) on biopsy, would you recommend completing evaluation for pulmonary sarcoidosis and neurosarcoidosis?
2 Answers
Mednet Member
Rheumatology · University of Alabama Birmingham
Presumably, the biopsy reveals non-caseating granulomas. Chronic dacryoadenitis can be seen in a variety of settings, including ANCA-associated vasculitis, Sjogren, IgG4-related disease, Crohn's disease, Lyme disease, tuberculosis, EBV, etc. Additional sarcoidosis workup will in part depend on other...
Mednet Member
Rheumatology · Hospital for Special Surgery/Weill Cornell Medicine
Writing as an adult rheumatologist, I agree with Dr. @Dr. First Last’s opinion that a chest x-ray, ophthalmologic screening for uveitis and close clinical monitoring for neurologic symptoms are appropriate in the described patient, but I do admit to being unaware of any phenotypic variants of pediat...