Is there any role for immunosuppressive therapy in patients with primary Sjogren's disease with severe pulmonary artery hypertension without ILD findings?

PAH (WHO Class I PH) in/and SJD is not a common relation, and as such would Rx as we Rx regarding PAH in PSS? The pathophysiology of PSS is, at least in part, a vasculopathy that SJD may not share. The question is, however, specific regarding Primary SJD and the assumption then is that this is not a...

I have a similar situation, a female in her mid 70s with severe pulmonary HTN on RHC, which is suggestive primarily of pre-capillary pulmonary HTN.

She has strongly elevated +SSB and SSA-60 with sxs of dry eyes. She has co-existing cirrhosis with portal HTN. Referred by pulm. She may have multiple e...