Mednet Logo
HomePrimary CareQuestion

How do you approach immunosuppressive therapy in lupus-associated pulmonary arterial hypertension?

1
2 Answers
Mednet Member
Mednet Member
Rheumatology · NYU Langone Health

I agree with Dr. @Dr. First Last that pulmonary arterial hypertension in SLE is infrequent. In the October issue of arthritis and rheumatology, the prevalence was 2.54% in a cohort of Chinese patients. Management requires distinguishing amongst the 5 WHO groups of PAH, which in lupus includes the fo...

Register or Sign In to see full answer

Mednet Member
Mednet Member
Rheumatology · Beth Israel Deaconess Medical Center

PAH is a rare manifestation in SLE. In our cohort, approximately 1.5% of SLE patients have been diagnosed with pulmonary hypertension. Half had interstitial lung disease and half were diagnosed as primary pulmonary hypertension. The therapeutic approach has been to address with immune suppressives t...

Register or Sign In to see full answer